EC20.02

ICD-11 MMS 2026-01

Autosomal recessive congenital ichthyosis

Description

A heterogeneous group of genetically-determined ichthyoses with autosomal recessive inheritance.

Index terms

  • Autosomal recessive congenital ichthyosis
  • Congenital non-bullous ichthyosiform erythroderma
  • Congenital ichthyotic ichthyosis
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  • Lamellar ichthyosis
  • Collodion baby
  • Congenital lamellar ichthyosis
  • Harlequin ichthyosis
  • Harlequin colour change syndrome
  • Self-healing collodion baby
  • Acral self-healing collodion baby
  • Bathing suit ichthyosis

Sibling codes

  • EC20.00 – Ichthyosis vulgaris
  • EC20.01 – X-linked ichthyosis
  • EC20.03 – Keratinopathic ichthyoses
  • EC20.0Y – Other specified or unclassifiable non-syndromic ichthyosis

Foundation entity

Autosomal recessive congenital ichthyosis – http://id.who.int/icd/entity/430849255

Part of: EC20.0: Non-syndromic ichthyosis › EC20: Genetic disorders of keratinisation › 14: Diseases of the skin