FB31.1

ICD-11 MMS 2026-01

Fibrodysplasia ossificans progressiva

Description

This is an extremely rare disease of the connective tissue where a mutation of the body's repair mechanism causes fibrous tissue (including muscle, tendon, and ligament) to be ossified when damaged.

Index terms

  • Fibrodysplasia ossificans progressiva
  • FOP - [fibrodysplasia ossificans progressiva]
  • Man of stone
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  • Myositis ossificans progressiva
  • Münchmeyer disease
  • diffuse progressive ossifying polymyositis
  • fibrodysplasia ossificans congenita
  • myositis ossificans progressiva, site unspecified
  • progressive myositis ossificans
  • progressive myositis ossificans calcification
  • Fibrodysplasia ossificans progressiva, multiple sites
  • Myositis ossificans progressiva, multiple sites
  • polymyositis ossificans
  • Fibrodysplasia ossificans progressiva, shoulder region
  • Myositis ossificans progressiva, shoulder region
  • Fibrodysplasia ossificans progressiva, acromioclavicular joint
  • Myositis ossificans progressiva, acromioclavicular joint
  • Fibrodysplasia ossificans progressiva, glenohumeral joint
  • Myositis ossificans progressiva, glenohumeral joint
  • Fibrodysplasia ossificans progressiva, sternoclavicular joint
  • Myositis ossificans progressiva, sternoclavicula joint
  • Fibrodysplasia ossificans progressiva, upper arm
  • Myositis ossificans progressiva, upper arm
  • Fibrodysplasia ossificans progressiva, elbow joint
  • Myositis ossificans progressiva, elbow joint
  • Fibrodysplasia ossificans progressiva, forearm
  • Myositis ossificans progressiva, forearm
  • Fibrodysplasia ossificans progressiva, wrist joint
  • Myositis ossificans progressiva, wrist joint
  • Fibrodysplasia ossificans progressiva, hand
  • Myositis ossificans progressiva, hand
  • Fibrodysplasia ossificans progressiva, carpus
  • Myositis ossificans progressiva, carpus
  • Fibrodysplasia ossificans progressiva, fingers
  • Myositis ossificans progressiva, fingers
  • Fibrodysplasia ossificans progressiva, metacarpus
  • Myositis ossificans progressiva, metacarpus
  • Fibrodysplasia ossificans progressiva, pelvic region or thigh
  • Myositis ossificans progressiva, pelvic region or thigh
  • Fibrodysplasia ossificans progressiva, buttock
  • Myositis ossificans progressiva, buttock
  • Fibrodysplasia ossificans progressiva, hip joint
  • Myositis ossificans progressiva, hip joint
  • Fibrodysplasia ossificans progressiva, lower leg
  • Myositis ossificans progressiva, lower leg
  • Fibrodysplasia ossificans progressiva, knee joint
  • Myositis ossificans progressiva, knee joint
  • Fibrodysplasia ossificans progressiva, ankle or foot
  • Myositis ossificans progressiva, ankle or foot
  • Fibrodysplasia ossificans progressiva, metatarsus
  • Myositis ossificans progressiva, metatarsus
  • Fibrodysplasia ossificans progressiva, tarsus
  • Myositis ossificans progressiva, tarsus
  • Fibrodysplasia ossificans progressiva, toes
  • Myositis ossificans progressiva, toes
  • Fibrodysplasia ossificans progressiva, ankle joint
  • Myositis ossificans progressiva, ankle joint
  • Fibrodysplasia ossificans progressiva, other joints in foot
  • Myositis ossificans progressiva, other joints in foot
  • Fibrodysplasia ossificans progressiva, head
  • Myositis ossificans progressiva, head
  • Fibrodysplasia ossificans progressiva, neck
  • Myositis ossificans progressiva, neck
  • Fibrodysplasia ossificans progressiva, vertebral column
  • Myositis ossificans progressiva, vertebral column
  • Myositis ossificans associated with dermatopolymyositis

Exclusions from above levels

  • 8C70 – Muscular dystrophy
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • DA0E.8 – Temporomandibular joint disorders

Sibling codes

  • FB31.0 – Progressive osseous heteroplasia
  • FB31.Y – Other specified calcification or ossification of muscle
  • FB31.Z – Calcification or ossification of muscle, unspecified

Foundation entity

Fibrodysplasia ossificans progressiva – http://id.who.int/icd/entity/2102976705

Part of: FB31: Calcification or ossification of muscle › 15: Diseases of the musculoskeletal system or connective tissue