GB90.44

ICD-11 MMS 2026-01

Renal tubular acidosis

Description

Conditions characterised by failure of the kidney to excrete acids, or to lose bicarbonate into the urine, which causes the blood to become too acidic. Characteristically hyperchloremic acidosis (low anion gap metabolic acidosis). Has several forms and many causes.

Index terms

  • Renal tubular acidosis
  • Lightwood syndrome
  • Lightwood-Albright syndrome
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  • RTA - [renal tubular acidosis]
  • idiopathic infantile hypercalcemia - mild form
  • kidney acidosis
  • kidney tubular acidosis
  • renal acidosis
  • renal hyperchloremic acidosis
  • renal tubule acidosis
  • Renal tubular acidosis - deafness
  • Autosomal recessive distal renal tubular acidosis with deafness
  • Acquired renal tubular acidosis
  • Renal tubular acidosis due to familial or genetic disorders
  • Type I renal tubular acidosis
  • Distal renal tubular acidosis
  • Distal renal tubular acidosis due to familial or genetic disease classified elsewhere
  • Distal Type 1 renal tubular acidosis due to familial and genetic disease classified elsewhere
  • Sporadic congenital renal tubular acidosis type 1
  • Autosomal dominant renal tubular acidosis type 1
  • Autosomal recessive renal tubular acidosis type 1
  • Renal tubular acidosis type 1 due to systemic disorders elsewhere classified
  • Acquired distal renal tubular acidosis
  • Acquired distal Type 1 renal tubular acidosis
  • Type II renal tubular acidosis
  • Proximal renal tubular acidosis
  • Proximal renal tubular acidosis due to familial or genetic disease
  • Proximal Type 2 renal tubular acidosis due to familial and genetic disease
  • Familial pure proximal renal tubular acidosis
  • Familial pure proximal Type 2 renal tubular acidosis
  • Proximal renal tubular acidosis with ocular abnormalities and intellectual deficit
  • Acquired proximal renal tubular acidosis with causes elsewhere classified
  • Acquired proximal Type 2 renal tubular acidosis with causes elsewhere classified
  • Type III renal tubular acidosis
  • Mixed proximal-distal renal tubular acidosis
  • Carbonic anhydrase II deficiency

Exclusions from above levels

  • http://id.who.int/icd/entity/1746821938 – Urolithiasis
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • GB90.40 – Hypotonia-cystinuria type 1
  • GB90.41 – Pseudohypoaldosteronism type 1
  • GB90.42 – Fanconi syndrome
  • GB90.43 – Bartter syndrome
  • GB90.45 – Renal glycosuria
  • GB90.46 – Tubular disorders of sodium or potassium transport
  • GB90.47 – Aminoaciduria
  • GB90.48 – Disorders of calcium or phosphate excretion
  • GB90.49 – Renal hypocalciuria
  • GB90.4A – Nephrogenic diabetes insipidus
  • GB90.4Y – Other specified renal tubular function disorders
  • GB90.4Z – Renal tubular function disorders, unspecified

Foundation entity

Renal tubular acidosis – http://id.who.int/icd/entity/1272869150

Part of: GB90.4: Renal tubular function disorders › GB90: Certain specified disorders of kidney or ureter › 16: Diseases of the genitourinary system