GB90.47

ICD-11 MMS 2026-01

Aminoaciduria

Description

Conditions in which amino acids are found in the urine either due to over-production (high blood levels) or failure of tubular resorption

Index terms

  • Aminoaciduria
  • Secondary aminoaciduria due to familial or genetic disorders
  • Aminoacidurias due to familial and genetic disorders elsewhere classified
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  • Primary inherited aminoaciduria
  • Acquired aminoaciduria associated with causes classified elsewhere

Exclusions from above levels

  • http://id.who.int/icd/entity/1746821938 – Urolithiasis
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • GB90.40 – Hypotonia-cystinuria type 1
  • GB90.41 – Pseudohypoaldosteronism type 1
  • GB90.42 – Fanconi syndrome
  • GB90.43 – Bartter syndrome
  • GB90.44 – Renal tubular acidosis
  • GB90.45 – Renal glycosuria
  • GB90.46 – Tubular disorders of sodium or potassium transport
  • GB90.48 – Disorders of calcium or phosphate excretion
  • GB90.49 – Renal hypocalciuria
  • GB90.4A – Nephrogenic diabetes insipidus
  • GB90.4Y – Other specified renal tubular function disorders
  • GB90.4Z – Renal tubular function disorders, unspecified

Foundation entity

Aminoaciduria – http://id.who.int/icd/entity/1360782719

Part of: GB90.4: Renal tubular function disorders › GB90: Certain specified disorders of kidney or ureter › 16: Diseases of the genitourinary system