LA02.02

ICD-11 MMS 2026-01

Myelocystocele

Description

A condition caused by failure of the neural tube to close completely during fetal development. The condition is characterised by skin covered lumbosacral masses, an arachnoid lined meningocele that is directly continuous with the spinal subarachnoid space, and a low lying hydromyelic spinal cord that traverses the meningocele and expands into a large terminal cyst. This condition can present with neural damage and consequent impairment of function below the site of the myelocystocele.

Index terms

  • Myelocystocele

Exclusions from above levels

  • LA03 – Arnold-Chiari malformation type II
  • LA07.4 – Arnold-Chiari malformation type I
  • LB73.0 – Occult spinal dysraphism
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  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA02.00 – Myelomeningocele with hydrocephalus
  • LA02.01 – Myelomeningocele without hydrocephalus
  • LA02.0Y – Other specified spina bifida cystica
  • LA02.0Z – Spina bifida cystica, unspecified

Foundation entity

Myelocystocele – http://id.who.int/icd/entity/863949070

Allowed postcoordination axes

Part of: LA02.0: Spina bifida cystica › LA02: Spina bifida › 20: Developmental anomalies