LA03

ICD-11 MMS 2026-01

Arnold-Chiari malformation type II

Description

A condition caused by failure of the brain and spinal cord to correctly develop during the antenatal period. This condition is characterised by extension of both cerebellar and brain stem tissue into the foramen magnum. This condition may present with partial or complete absence of the cerebellar vermis, myelomeningocele, neck pain, balance problems, muscle weakness, limb numbness, dizziness, vision problems, difficulty swallowing, ringing in the ears, hearing loss, vomiting, insomnia, depression, or impairment of motor skills.

Index terms

  • Arnold-Chiari malformation type II
  • Arnold-Chiari malformation NOS
  • Arnold-Chiari obstruction type II
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  • Arnold-Chiari syndrome NOS
  • Chiari malformation type II

Excludes

  • LA07.4 – Arnold-Chiari malformation type I

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA00 – Anencephaly or similar anomalies
  • LA01 – Cephalocele
  • LA02 – Spina bifida
  • LA04 – Congenital hydrocephalus
  • LA05 – Cerebral structural developmental anomalies
  • LA06 – Cerebellar structural developmental anomalies
  • LA07 – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
  • LA0Y – Other specified structural developmental anomalies of the nervous system
  • LA0Z – Structural developmental anomalies of the nervous system, unspecified

Foundation entity

Arnold-Chiari malformation type II – http://id.who.int/icd/entity/1987349422

Allowed postcoordination axes

Part of: 20: Developmental anomalies