Arnold-Chiari malformation type I

Description

A condition caused by failure of the cerebellum to correctly develop during the antenatal period. This condition is characterised by extension of the cerebellar tonsils into the foramen magnum, without involving the brain stem. This condition may present as asymptomatic. Confirmation is through observation of the cerebellar tonsil extension by imaging.

Index terms

Arnold-Chiari malformation type I
Arnold-Chiari obstruction type I
Chiari malformation type I

Excludes

LA03 – Arnold-Chiari malformation type II

Exclusions from above levels

http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA07.0 – Primary tethered cord syndrome
LA07.1 – Diastematomyelia
LA07.2 – Amyelia
LA07.3 – Primary syringomyelia or hydromyelia
LA07.Y – Other specified structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
LA07.Z – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column, unspecified

Foundation entity

Arnold-Chiari malformation type I – http://id.who.int/icd/entity/1383121646

Allowed postcoordination axes

hasManifestation

Part of: LA07: Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column › 20: Developmental anomalies