LA05.0

ICD-11 MMS 2026-01

Microcephaly

Description

A condition caused by failure of the head to correctly develop during the antenatal period. This condition is characterised by a head size that is significantly smaller than normal for their age and sex. This condition may also present with developmental delays, difficulties with balance and coordination, short stature, hyperactivity, mental retardation, seizures, or other neurological abnormalities.

Index terms

  • Microcephaly
  • Micrencephalon
  • Micrencephaly
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  • Microencephaly
  • brain hypoplasia
  • brain nondevelopment
  • cephalic hypoplasia
  • congenital microcephaly
  • microcephalic
  • microcephalus
  • nanocephaly
  • undeveloped brain
  • undeveloped cerebrum
  • Congenital skull deformity with microcephaly
  • absence of skull bone with microcephaly
  • anomaly of skull with microcephaly
  • skull agenesis with microcephaly
  • Hydromicrocephaly
  • Autosomal dominant primary microcephaly

Inclusions

  • Micrencephaly

Excludes

  • LD20.2 – Syndromes with microcephaly as a major feature

Exclusions from above levels

  • LA01 – Encephalocele
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA05.1 – Megalencephaly
  • LA05.2 – Holoprosencephaly
  • LA05.3 – Corpus callosum agenesis
  • LA05.4 – Arrhinencephaly
  • LA05.5 – Abnormal neuronal migration
  • LA05.6 – Encephaloclastic disorders
  • LA05.7 – Brain cystic malformations
  • LA05.8 – Colpocephaly
  • LA05.Y – Other specified cerebral structural developmental anomalies
  • LA05.Z – Cerebral structural developmental anomalies, unspecified

Foundation entity

Microcephaly – http://id.who.int/icd/entity/179350437

Allowed postcoordination axes

Part of: LA05: Cerebral structural developmental anomalies › 20: Developmental anomalies