LA05.7

ICD-11 MMS 2026-01

Brain cystic malformations

Description

A disease caused by expansion of the roof plate of the brain vesicle, or by extraaxial structures such as an arachnoid membrane or migrating ependymal cells. This disease is characterised by the presence of fluid filled cysts in the brain. This disease may present with asymmetry of the skull, brain compression, raised intracranial pressure, hydrocephalus, bleeding or seizures. This disease may also be asymptomatic. Confirmation is through observation of intracerebral cysts by imaging.

Index terms

  • Brain cystic malformations
  • Congenital cerebral cysts
  • congenital brain cyst
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  • congenital cerebral porosis
  • congenital cystic brain degeneration
  • Glioependymal or ependymal cysts
  • Choroid plexus cysts
  • cyst of choroid plexus
  • Congenital brain third ventricle colloid cyst
  • congenital third ventricle brain cyst

Excludes

  • 8E40.Y – Acquired porencephalic cysts
  • LA06.0 – Dandy-Walker malformation without hydrocephalus

Exclusions from above levels

  • LA01 – Encephalocele
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Foundation children elsewhere

  • 8D67 – Intracranial arachnoid cyst

Sibling codes

  • LA05.0 – Microcephaly
  • LA05.1 – Megalencephaly
  • LA05.2 – Holoprosencephaly
  • LA05.3 – Corpus callosum agenesis
  • LA05.4 – Arrhinencephaly
  • LA05.5 – Abnormal neuronal migration
  • LA05.6 – Encephaloclastic disorders
  • LA05.8 – Colpocephaly
  • LA05.Y – Other specified cerebral structural developmental anomalies
  • LA05.Z – Cerebral structural developmental anomalies, unspecified

Foundation entity

Brain cystic malformations – http://id.who.int/icd/entity/1633056148

Part of: LA05: Cerebral structural developmental anomalies › 20: Developmental anomalies