LA06.0

ICD-11 MMS 2026-01

Dandy-Walker malformation

Description

Dandy-Walker malformation is the association of three signs: hydrocephalus, partial or complete absence of the cerebellar vermis, and posterior fossa cyst contiguous with the fourth ventricle.

Index terms

  • Dandy-Walker malformation
  • Dandy Walker cyst
  • Dandy-Walker deformity
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  • Dandy-Walker syndrome
  • atresia of foramen of Luschka
  • atresia of foramen of Magendie
  • congenital blockage of foramen Magendie
  • Dandy-Walker malformation with hydrocephalus
  • congenital blocked foramen Magendie with hydrocephalus
  • Dandy-Walker malformation without hydrocephalus
  • Cystic cerebrospinal fluid collection due to Dandy walker malformation

Exclusions from above levels

  • LA03 – Arnold-Chiari malformation type II
  • LA07.4 – Arnold-Chiari malformation type I
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA06.1 – Hypoplasia or agenesis of cerebellar hemispheres
  • LA06.2 – Focal cerebellar dysplasia
  • LA06.Y – Other specified cerebellar structural developmental anomalies
  • LA06.Z – Cerebellar structural developmental anomalies, unspecified

Foundation entity

Dandy-Walker malformation – http://id.who.int/icd/entity/993088960

Allowed postcoordination axes

Part of: LA06: Cerebellar structural developmental anomalies › 20: Developmental anomalies