LA87.40

ICD-11 MMS 2026-01

Atrioventricular septal defect with communication at the atrial level only

Description

A congenital cardiac malformation that is a variant of an atrioventricular septal defect (atrioventricular canal defect) with an interatrial communication just above the atrioventricular valve, no interventricular communication just below the atrioventricular valve, separate right and left atrioventricular valvar orifices, and varying degrees of malformation of the left sided component of the common atrioventricular valve. Additional information: the bridging leaflets of the common atrioventricular valve are bound down to the crest of the scooped out ventricular septum so that the potential for shunting through the atrioventricular septal defect is possible only at the atrial level and not at the ventricular level.

Index terms

  • Atrioventricular septal defect with communication at the atrial level only
  • atrial septum primum defect
  • atrioventricular defect with atrial shunting only
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  • incomplete atrioventricular canal defect with isolated atrial component
  • incomplete atrioventricular septal defect with isolated atrial component
  • ostium primum atrial septal defect
  • partial atrioventricular canal defect
  • partial atrioventricular canal defect with isolated atrial component
  • partial atrioventricular septal defect
  • partial atrioventricular septal defect, ostium primum type
  • primum atrial septal defect

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA87.41 – Atrioventricular septal defect with communication at the ventricular level only
  • LA87.42 – Atrioventricular septal defect with communication at atrial level and restrictive communication at ventricular level
  • LA87.43 – Atrioventricular septal defect with communication at atrial level and unrestrictive communication at ventricular level
  • LA87.44 – Atrioventricular septal defect with ventricular imbalance
  • LA87.45 – Atrioventricular septal defect and tetralogy of Fallot
  • LA87.4Y – Other specified common atrioventricular junction with atrioventricular septal defect
  • LA87.4Z – Common atrioventricular junction with atrioventricular septal defect, unspecified

Foundation entity

Atrioventricular septal defect with communication at the atrial level only – http://id.who.int/icd/entity/1159570489

Part of: LA87.4: Common atrioventricular junction with atrioventricular septal defect › LA87: Congenital anomaly of an atrioventricular valve or atrioventricular septum › 20: Developmental anomalies