LA87.42

ICD-11 MMS 2026-01

Atrioventricular septal defect with communication at atrial level and restrictive communication at ventricular level

Description

A congenital cardiac malformation that is a variant of an atrioventricular septal defect (atrioventricular canal defect) with an interatrial communication immediately above the atrioventricular valve, and a restrictive interventricular communication immediately below the atrioventricular valve.

Index terms

  • Atrioventricular septal defect with communication at atrial level and restrictive communication at ventricular level
  • atrioventricular canal defect associated with a restrictive ventricular septal defect
  • atrioventricular septal defect with atrial shunting and restrictive ventricular shunting
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  • intermediate atrioventricular canal defect
  • intermediate atrioventricular canal defect with atrial and ventricular components and separate atrioventricular valve
  • intermediate atrioventricular septal defect
  • intermediate atrioventricular septal defect with atrial and ventricular components and separate atrioventricular valvar orifices
  • transitional atrioventricular canal defect
  • transitional atrioventricular septal defect
  • transitional atrioventricular septal defect with atrial and ventricular components and separate atrioventricular valves

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA87.40 – Atrioventricular septal defect with communication at the atrial level only
  • LA87.41 – Atrioventricular septal defect with communication at the ventricular level only
  • LA87.43 – Atrioventricular septal defect with communication at atrial level and unrestrictive communication at ventricular level
  • LA87.44 – Atrioventricular septal defect with ventricular imbalance
  • LA87.45 – Atrioventricular septal defect and tetralogy of Fallot
  • LA87.4Y – Other specified common atrioventricular junction with atrioventricular septal defect
  • LA87.4Z – Common atrioventricular junction with atrioventricular septal defect, unspecified

Foundation entity

Atrioventricular septal defect with communication at atrial level and restrictive communication at ventricular level – http://id.who.int/icd/entity/687321516

Part of: LA87.4: Common atrioventricular junction with atrioventricular septal defect › LA87: Congenital anomaly of an atrioventricular valve or atrioventricular septum › 20: Developmental anomalies