LA87.44

ICD-11 MMS 2026-01

Atrioventricular septal defect with ventricular imbalance

Description

A congenital cardiac malformation that is a variant of an atrioventricular septal defect (atrioventricular canal defect) with one ventricle significantly larger than the other. Additional information: unbalanced ventricular size and unbalanced relation of the common atrioventricular valve to the ventricles are to be distinguished by coding unbalanced ventricular size as 'Atrioventricular septal defect with ventricular imbalance' and the unbalanced relation of the common atrioventricular valve to the ventricles should also be coded as 'Common atrioventricular valve with unbalanced commitment of valve to ventricles'.

Index terms

  • Atrioventricular septal defect with ventricular imbalance
  • Atrioventricular septal defect with ventricular imbalance with dominant right ventricle and hypoplastic left ventricle
  • complete atrioventricular septal defect with left ventricular hypoplasia
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  • Atrioventricular septal defect with ventricular imbalance with dominant left ventricle and hypoplastic right ventricle
  • complete atrioventricular septal defect with right ventricular hypoplasia

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA87.40 – Atrioventricular septal defect with communication at the atrial level only
  • LA87.41 – Atrioventricular septal defect with communication at the ventricular level only
  • LA87.42 – Atrioventricular septal defect with communication at atrial level and restrictive communication at ventricular level
  • LA87.43 – Atrioventricular septal defect with communication at atrial level and unrestrictive communication at ventricular level
  • LA87.45 – Atrioventricular septal defect and tetralogy of Fallot
  • LA87.4Y – Other specified common atrioventricular junction with atrioventricular septal defect
  • LA87.4Z – Common atrioventricular junction with atrioventricular septal defect, unspecified

Foundation entity

Atrioventricular septal defect with ventricular imbalance – http://id.who.int/icd/entity/560731030

Part of: LA87.4: Common atrioventricular junction with atrioventricular septal defect › LA87: Congenital anomaly of an atrioventricular valve or atrioventricular septum › 20: Developmental anomalies