LA8A.1

ICD-11 MMS 2026-01

Congenital pulmonary atresia

Description

A congenital cardiovascular malformation in which there is no opening between any ventricle and the pulmonary arterial tree.

Excludes

  • LA88.21 – Tetralogy of Fallot with pulmonary atresia

Exclusions from above levels

  • LA85.4 – Common arterial trunk
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Child codes

  • LA8A.10 – Pulmonary atresia with intact ventricular septum
  • LA8A.1Y – Other specified congenital pulmonary atresia
  • LA8A.1Z – Congenital pulmonary atresia, unspecified

Sibling codes

  • LA8A.0 – Congenital anomaly of pulmonary valve
  • LA8A.2 – Congenital anomaly of aortic valve
  • LA8A.3 – Congenital supravalvar aortic stenosis
  • LA8A.4 – Aneurysm of aortic sinus of Valsalva
  • LA8A.5 – Congenital subaortic stenosis
  • LA8A.6 – Congenital subpulmonary stenosis
  • LA8A.Y – Other specified congenital anomaly of a ventriculo-arterial valve or adjacent regions
  • LA8A.Z – Congenital anomaly of a ventriculo-arterial valve or adjacent regions, unspecified

Foundation entity

Congenital pulmonary atresia – http://id.who.int/icd/entity/1883690033

Part of: LA8A: Congenital anomaly of a ventriculo-arterial valve or adjacent regions › 20: Developmental anomalies