Congenital subpulmonary stenosis

Description

A congenital cardiovascular malformation associated with narrowing within the outflow tract supporting the pulmonary valve. Additional information: subvalvar (infundibular) pulmonary stenosis is a narrowing of the outflow tract of the ventricle immediately below the pulmonic valve. This term should preferably be used in the setting of abnormal ventriculo-arterial connections, such as double outlet ventricle. Although subvalvar pulmonary stenosis is a type of right ventricular outflow tract obstruction if the ventriculo-arterial connections are normal, in this setting 'Congenital right ventricular outflow tract obstruction' should be used. Subvalvar pulmonary stenosis is also a type of left ventricular outflow tract obstruction in the setting of discordant ventriculo-arterial connections; this term should be used when the obstruction is only apparent immediately below the pulmonary valve, otherwise the term 'Congenital left ventricular outflow tract obstruction' should be used

Index terms

Congenital subpulmonary stenosis
infundibular pulmonary stenosis

Excludes

LA88.1 – Double chambered right ventricle

Exclusions from above levels

LA85.4 – Common arterial trunk
http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

LA8A.0 – Congenital anomaly of pulmonary valve
LA8A.1 – Congenital pulmonary atresia
LA8A.2 – Congenital anomaly of aortic valve
LA8A.3 – Congenital supravalvar aortic stenosis
LA8A.4 – Aneurysm of aortic sinus of Valsalva
LA8A.5 – Congenital subaortic stenosis
LA8A.Y – Other specified congenital anomaly of a ventriculo-arterial valve or adjacent regions
LA8A.Z – Congenital anomaly of a ventriculo-arterial valve or adjacent regions, unspecified

Foundation entity

Congenital subpulmonary stenosis – http://id.who.int/icd/entity/1393194578

Part of: LA8A: Congenital anomaly of a ventriculo-arterial valve or adjacent regions › 20: Developmental anomalies