LA90.5

ICD-11 MMS 2026-01

Pulmonary arteriovenous fistula

Description

A congenital cardiovascular malformation in which there is an abnormal, direct connection between a pulmonary artery and pulmonary vein or left atrium without an intervening capillary bed.

Index terms

  • Pulmonary arteriovenous fistula
  • Pulmonary arteriovenous aneurysm
  • Pulmonary arteriovenous malformation

Exclusions from above levels

  • 2E81 – haemangioma and lymphangioma
  • LA13.5 – Congenital retinal aneurysm
  • LA8B.1 – Congenital anomaly of pulmonary arterial tree
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  • LA8C – Congenital anomaly of coronary artery
  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA90.0 – Capillary malformations
  • LA90.1 – Lymphatic malformations
  • LA90.2 – Peripheral venous malformations
  • LA90.3 – Peripheral arteriovenous malformations
  • LA90.4 – Peripheral arterial malformations
  • LA90.Y – Other specified structural developmental anomalies of the peripheral vascular system
  • LA90.Z – Structural developmental anomalies of the peripheral vascular system, unspecified

Foundation entity

Pulmonary arteriovenous fistula – http://id.who.int/icd/entity/913404991

Part of: LA90: Structural developmental anomalies of the peripheral vascular system › 20: Developmental anomalies