LB31.0

ICD-11 MMS 2026-01

Congenital hydronephrosis

Description

Congenital hydronephrosis is a renal urinary disease characterised by distension and dilation of the renal pelvis and calyces secondary to various congenital obstructive malformations of the kidneys and urinary tract that can evolve to renal atrophy.

Index terms

  • Congenital hydronephrosis
  • congenital hydrocalycosis
  • congenital hydroureteronephrosis
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  • Congenital primary hydronephrosis
  • Congenital primary hydronephrosis, unilateral
  • Congenital primary hydronephrosis, bilateral
  • Congenital secondary hydronephrosis
  • Congenital secondary hydronephrosis, unilateral
  • Congenital secondary hydronephrosis, bilateral

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB31.1 – Congenital primary megaureter
  • LB31.2 – Fetal lower urinary tract obstruction
  • LB31.3 – Exstrophy of urinary bladder
  • LB31.4 – Congenital diverticulum of urinary bladder
  • LB31.5 – Duplication of urethra
  • LB31.6 – Congenital megalourethra
  • LB31.7 – Megacystis-megaureter
  • LB31.8 – Atresia or stenosis of ureter
  • LB31.9 – Agenesis of ureter
  • LB31.A – Duplication of ureter
  • LB31.B – Malposition of ureter
  • LB31.C – Congenital absence of bladder or urethra
  • LB31.D – Congenital vesico-uretero-renal reflux
  • LB31.Y – Other specified structural developmental anomalies of urinary tract
  • LB31.Z – Structural developmental anomalies of urinary tract, unspecified

Foundation entity

Congenital hydronephrosis – http://id.who.int/icd/entity/808343797

Allowed postcoordination axes

Part of: LB31: Structural developmental anomalies of urinary tract › 20: Developmental anomalies