LB31.A

ICD-11 MMS 2026-01

Duplication of ureter

Description

A condition caused by failure of the ureter to correctly develop during the antenatal period, resulting in incorrect connection of the ureter to the kidney. This condition may present with ureteroureteral reflux, or ureteropelvic junction obstruction of the lower pole of the kidney in the case of incomplete duplication. Complete duplication may present with vesicoureteral reflux, ectopic ureterocele, or ectopic ureteral insertion. Confirmation is through observation of two ureters on one side by imaging.

Index terms

  • Duplication of ureter
  • Accessory ureter
  • Double ureter
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  • bifid ureter
  • ureter bifurcation
  • Double ureter with double pelvis

Inclusions

  • Accessory ureter
  • Double ureter

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB31.0 – Congenital hydronephrosis
  • LB31.1 – Congenital primary megaureter
  • LB31.2 – Fetal lower urinary tract obstruction
  • LB31.3 – Exstrophy of urinary bladder
  • LB31.4 – Congenital diverticulum of urinary bladder
  • LB31.5 – Duplication of urethra
  • LB31.6 – Congenital megalourethra
  • LB31.7 – Megacystis-megaureter
  • LB31.8 – Atresia or stenosis of ureter
  • LB31.9 – Agenesis of ureter
  • LB31.B – Malposition of ureter
  • LB31.C – Congenital absence of bladder or urethra
  • LB31.D – Congenital vesico-uretero-renal reflux
  • LB31.Y – Other specified structural developmental anomalies of urinary tract
  • LB31.Z – Structural developmental anomalies of urinary tract, unspecified

Foundation entity

Duplication of ureter – http://id.who.int/icd/entity/1378244108

Allowed postcoordination axes

Part of: LB31: Structural developmental anomalies of urinary tract › 20: Developmental anomalies