LB31.6

ICD-11 MMS 2026-01

Congenital megalourethra

Description

A condition caused by failure of the penile corpora cavernosa and spongiosa to correctly develop during the antenatal period. This condition is characterised by dilatation of the penile urethra. This condition may present with poor stream, swelling of the penis, megacystis, oligohydramnios, renal failure, or pulmonary hypoplasia.

Index terms

  • Congenital megalourethra

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LB31.0 – Congenital hydronephrosis
  • LB31.1 – Congenital primary megaureter
  • LB31.2 – Fetal lower urinary tract obstruction
  • LB31.3 – Exstrophy of urinary bladder
  • LB31.4 – Congenital diverticulum of urinary bladder
  • LB31.5 – Duplication of urethra
  • LB31.7 – Megacystis-megaureter
  • LB31.8 – Atresia or stenosis of ureter
  • LB31.9 – Agenesis of ureter
  • LB31.A – Duplication of ureter
  • LB31.B – Malposition of ureter
  • LB31.C – Congenital absence of bladder or urethra
  • LB31.D – Congenital vesico-uretero-renal reflux
  • LB31.Y – Other specified structural developmental anomalies of urinary tract
  • LB31.Z – Structural developmental anomalies of urinary tract, unspecified

Foundation entity

Congenital megalourethra – http://id.who.int/icd/entity/1253018132

Part of: LB31: Structural developmental anomalies of urinary tract › 20: Developmental anomalies