Atypical chronic myeloid leukaemia, BCR-ABL1-negative

Description

A myelodysplastic/myeloproliferative neoplasm characterised by the principal involvement of the neutrophil series with leukocytosis with circulating immature myeloid cells, fewer than 20 percent blasts in the bone marrow and blood, and severe dysgranulopoiesis. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL1 fusion gene.

Index terms

Atypical chronic myeloid leukaemia, BCR-ABL1-negative
Atypical chronic myeloid leukaemia, BCR-ABL-negative without mention of remission
atypical chronic myeloid leukaemia

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subacute monocytic leukaemia
subacute monocytic leukaemia without mention of remission
subacute myelogenous leukaemia
subacute myeloid leukaemia
subacute myelosis
Atypical chronic myeloid leukaemia, BCR-ABL1-negative in complete remission

Exclusions from above levels

2E03 – Malignant neoplasm metastasis in bone or bone marrow
http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

2A40 – Chronic myelomonocytic leukaemia
2A42 – Juvenile myelomonocytic leukaemia
2A43 – Refractory anaemia with ring sideroblasts associated with marked thrombocytosis
2A44 – Myeloproliferative and myelodysplastic disease, unclassifiable
2A4Y – Other specified myelodysplastic and myeloproliferative neoplasms
2A4Z – Myelodysplastic and myeloproliferative neoplasms, unspecified

Foundation entity

Atypical chronic myeloid leukaemia, BCR-ABL1-negative – http://id.who.int/icd/entity/331838766

Allowed postcoordination axes

Part of: 02: Neoplasms