2A43

ICD-11 MMS 2026-01

Refractory anaemia with ring sideroblasts associated with marked thrombocytosis

Description

A provisional entity that encompasses cases with morphologic and clinical characteristics of refractory anaemia with ring sideroblasts, marked thrombocytosis, and abnormal megakaryocytes.

Index terms

  • Refractory anaemia with ring sideroblasts associated with marked thrombocytosis
  • RARS-T [Refractory anaemia with ringed sideroblasts associated with marked thrombocytosis](provisional)

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A40 – Chronic myelomonocytic leukaemia
  • 2A41 – Atypical chronic myeloid leukaemia, BCR-ABL1-negative
  • 2A42 – Juvenile myelomonocytic leukaemia
  • 2A44 – Myeloproliferative and myelodysplastic disease, unclassifiable
  • 2A4Y – Other specified myelodysplastic and myeloproliferative neoplasms
  • 2A4Z – Myelodysplastic and myeloproliferative neoplasms, unspecified

Foundation entity

Refractory anaemia with ring sideroblasts associated with marked thrombocytosis – http://id.who.int/icd/entity/211329077

Allowed postcoordination axes

Part of: 02: Neoplasms