2B31.0

ICD-11 MMS 2026-01

Juvenile xanthogranuloma

Description

It is characterised by the presence of lipid-laden, foamy histiocytes and Touton-type giant cells in the dermis.

Index terms

  • Juvenile xanthogranuloma
  • Cutaneous juvenile xanthogranuloma
  • Disseminated juvenile xanthogranuloma
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  • Ocular juvenile xanthogranuloma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B31.1 – Histiocytic sarcoma
  • 2B31.2 – Langerhans cell histiocytosis
  • 2B31.3 – Langerhans cell sarcoma
  • 2B31.4 – Interdigitating dendritic cell sarcoma
  • 2B31.5 – Follicular dendritic cell sarcoma
  • 2B31.6 – Indeterminate cell histiocytosis
  • 2B31.7 – Fibroblastic reticular cell tumour
  • 2B31.Y – Other specified histiocytic or dendritic cell neoplasms
  • 2B31.Z – Histiocytic or dendritic cell neoplasms, unspecified

Foundation entity

Juvenile xanthogranuloma – http://id.who.int/icd/entity/98595592

Allowed postcoordination axes

Part of: 2B31: Histiocytic or dendritic cell neoplasms › 02: Neoplasms