2B31.7

ICD-11 MMS 2026-01

Fibroblastic reticular cell tumour

Description

A very rare dendritic cell tumour affecting the lymph nodes, spleen, and soft tissues. Morphologically it is similar to the interdigitating dendritic cell sarcoma or follicular dendritic cell sarcoma. The tumour cells are positive for cytokeratin and CD68. Clinical outcome is variable.

Index terms

  • Fibroblastic reticular cell tumour

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B31.0 – Juvenile xanthogranuloma
  • 2B31.1 – Histiocytic sarcoma
  • 2B31.2 – Langerhans cell histiocytosis
  • 2B31.3 – Langerhans cell sarcoma
  • 2B31.4 – Interdigitating dendritic cell sarcoma
  • 2B31.5 – Follicular dendritic cell sarcoma
  • 2B31.6 – Indeterminate cell histiocytosis
  • 2B31.Y – Other specified histiocytic or dendritic cell neoplasms
  • 2B31.Z – Histiocytic or dendritic cell neoplasms, unspecified

Foundation entity

Fibroblastic reticular cell tumour – http://id.who.int/icd/entity/357570888

Allowed postcoordination axes

Part of: 2B31: Histiocytic or dendritic cell neoplasms › 02: Neoplasms