2B31

ICD-11 MMS 2026-01

Histiocytic or dendritic cell neoplasms

Description

True histiocytic malignancies are vanishing diagnoses due to improved understanding of the provenance of malignant cells.

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Child codes

  • 2B31.0 – Juvenile xanthogranuloma
  • 2B31.1 – Histiocytic sarcoma
  • 2B31.2 – Langerhans cell histiocytosis
  • 2B31.3 – Langerhans cell sarcoma
  • 2B31.4 – Interdigitating dendritic cell sarcoma
  • 2B31.5 – Follicular dendritic cell sarcoma
  • 2B31.6 – Indeterminate cell histiocytosis
  • 2B31.7 – Fibroblastic reticular cell tumour
  • 2B31.Y – Other specified histiocytic or dendritic cell neoplasms
  • 2B31.Z – Histiocytic or dendritic cell neoplasms, unspecified

Sibling codes

  • 2A60 – Acute myeloid leukaemias and related precursor neoplasms
  • 2A61 – Acute leukaemias of ambiguous lineage
  • 2B30 – Hodgkin lymphoma
  • 2B32 – Immunodeficiency-associated lymphoproliferative disorders
  • 2B33 – Malignant haematopoietic neoplasms without further specification
  • 2B3Z – Neoplasms of haematopoietic or lymphoid tissues, unspecified

Foundation entity

Histiocytic or dendritic cell neoplasms – http://id.who.int/icd/entity/2022303330

Allowed postcoordination axes

Part of: 02: Neoplasms