2B31.5

ICD-11 MMS 2026-01

Follicular dendritic cell sarcoma

Description

A neoplasm composed of spindle to ovoid cells which have morphologic and immunophenotypic characteristics of follicular dendritic cells. It affects lymph nodes and other sites including the tonsils, gastrointestinal tract, spleen, liver, soft tissues, skin, and oral cavity. It usually behaves as a low grade sarcoma. Recurrences have been reported in up to half of the cases.

Index terms

  • Follicular dendritic cell sarcoma

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2B31.0 – Juvenile xanthogranuloma
  • 2B31.1 – Histiocytic sarcoma
  • 2B31.2 – Langerhans cell histiocytosis
  • 2B31.3 – Langerhans cell sarcoma
  • 2B31.4 – Interdigitating dendritic cell sarcoma
  • 2B31.6 – Indeterminate cell histiocytosis
  • 2B31.7 – Fibroblastic reticular cell tumour
  • 2B31.Y – Other specified histiocytic or dendritic cell neoplasms
  • 2B31.Z – Histiocytic or dendritic cell neoplasms, unspecified

Foundation entity

Follicular dendritic cell sarcoma – http://id.who.int/icd/entity/15445528

Allowed postcoordination axes

Part of: 2B31: Histiocytic or dendritic cell neoplasms › 02: Neoplasms