3B14.1

ICD-11 MMS 2026-01

Hereditary factor X deficiency

Description

Congenital factor X deficiency is an inherited bleeding disorder with a decreased antigen and/or activity of factor X (FX) and characterised by mild to severe bleeding symptoms.

Index terms

  • Hereditary factor X deficiency
  • Congenital Stuart factor deficiency
  • Deficiency of factor X
Show allHide
  • Stuart Prower deficiency
  • Stuart deficiency disease
  • Stuart-Prower disease
  • Stuart-Prower factor deficiency
  • congenital factor x deficiency

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
Show allHide
  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B14.0 – Hereditary deficiency of factor I
  • 3B14.2 – Combined deficiency of vitamin K-dependent clotting factors
  • 3B14.Z – Other inherited coagulation factor deficiency with bleeding tendency, unspecified

Foundation entity

Hereditary factor X deficiency – http://id.who.int/icd/entity/1886781445

Part of: 3B14: Other inherited coagulation factor deficiency with bleeding tendency › 03: Diseases of the blood or blood-forming organs