3B14.1ICD-11 MMS 2026-01
Hereditary factor X deficiency
Description
Congenital factor X deficiency is an inherited bleeding disorder with a decreased antigen and/or activity of factor X (FX) and characterised by mild to severe bleeding symptoms.
Index terms
- Hereditary factor X deficiency
- Congenital Stuart factor deficiency
- Deficiency of factor X
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- Stuart Prower deficiency
- Stuart deficiency disease
- Stuart-Prower disease
- Stuart-Prower factor deficiency
- congenital factor x deficiency
Exclusions from above levels
JA43.3– Postpartum coagulation defects04– Diseases of the immune system05– Endocrine, nutritional or metabolic diseases
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18– Complications of pregnancy, childbirth or the puerperium19– Certain conditions originating in the perinatal period20– Congenital malformations, deformations or chromosomal abnormalities22– Injury, poisoning or certain other consequences of external causes- http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
JB64.1– Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium
Sibling codes
Foundation entity
Hereditary factor X deficiency – http://id.who.int/icd/entity/1886781445
Part of: 3B14: Other inherited coagulation factor deficiency with bleeding tendency › 03: Diseases of the blood or blood-forming organs