3B22

ICD-11 MMS 2026-01

Acquired haemophilia

Description

Acquired haemophilia is a rare haemorrhagic disease caused by production of anti-factor VIII antibodies and is sometimes associated with other autoimmune disorders, cancers, lymphoproliferative syndromes and multiple transfusions during the postpartum period.

Index terms

  • Acquired haemophilia
  • Autoimmune coagulation factor deficiency
  • nonfamilial haemophilia
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  • Acquired haemophilia A
  • Acquired haemophilia B
  • Acquired factor XIII deficiency

Exclusions from above levels

  • KA8F.0 – vitamin K deficiency of newborn
  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B20 – Disseminated intravascular coagulation
  • 3B21 – Haemorrhagic disorder due to circulating anticoagulants or coagulation factors inhibitors
  • 3B2Y – Other specified haemorrhagic diseases due to acquired coagulation factor defects

Foundation entity

Acquired haemophilia – http://id.who.int/icd/entity/1559879199

Allowed postcoordination axes

Part of: 03: Diseases of the blood or blood-forming organs