3B20

ICD-11 MMS 2026-01

Disseminated intravascular coagulation

Description

A disorder that is characterised by the systemic intravascular activation of the coagulation system, simultaneously leading to intravascular thrombi, compromising an adequate blood supply to the organs, and to bleeding as the consequence of consumption of platelets and coagulation factors. It may be provoked by a wide range of disorders including infections, inflammatory disorders and malignancy.

Index terms

  • Disseminated intravascular coagulation
  • Consumption coagulopathy
  • DIC - [disseminated intravascular coagulation]
Show allHide
  • Defibrination syndrome
  • Diffuse intravascular coagulation
  • Fibrinolytic purpura
  • disseminated intravascular coagulopathy
  • fibrinolysis NOS
  • thrombolytic purpura
  • Purpura fulminans
  • Acquired fibrinolytic haemorrhage
  • haemorrhagic fibrinolysis
  • Gangrenous purpura
  • Acquired hypofibrinogenaemia
  • acquired afibrinogenaemia
  • acquired fibrinogenopenia

Exclusions from above levels

  • KA8F.0 – vitamin K deficiency of newborn
  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
Show allHide
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Foundation children elsewhere

  • KA88 – Disseminated intravascular coagulation of fetus or newborn

Sibling codes

  • 3B21 – Haemorrhagic disorder due to circulating anticoagulants or coagulation factors inhibitors
  • 3B22 – Acquired haemophilia
  • 3B2Y – Other specified haemorrhagic diseases due to acquired coagulation factor defects

Foundation entity

Disseminated intravascular coagulation – http://id.who.int/icd/entity/1622289887

Part of: 03: Diseases of the blood or blood-forming organs