3B2Y

ICD-11 MMS 2026-01

Other specified haemorrhagic diseases due to acquired coagulation factor defects

Inclusions

  • Deficiency of coagulation factor due to vitamin K deficiency
  • Acquired von Willebrand disease
  • Acquired prothrombin complex deficiency
  • Deficiency of coagulation factor due to liver disease

Exclusions from above levels

  • KA8F.0 – vitamin K deficiency of newborn
  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B20 – Disseminated intravascular coagulation
  • 3B21 – Haemorrhagic disorder due to circulating anticoagulants or coagulation factors inhibitors
  • 3B22 – Acquired haemophilia

Foundation entity

Haemorrhagic diseases due to acquired coagulation factor defects – http://id.who.int/icd/entity/2057381685

Part of: 03: Diseases of the blood or blood-forming organs