Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells

Description

This refers to a nonfamilial type of primary immune deficiency disease characterised by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells may be normal or low.

Index terms

Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
Hypogammaglobulinaemia NOS
acquired agammaglobulinaemia NOS

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agammaglobulinaemia NOS
agammaglobulinaemia antibody deficiency syndrome
common variable agammaglobulinaemia
hypogammaglobulinaemia antibody deficiency syndrome
nonfamilial agammaglobulinaemia
nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
immunoglobulin-bearing b-lymphocytes agammaglobulinaemia

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A01.00 – Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
4A01.02 – Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
4A01.03 – Transient hypogammaglobulinaemia of infancy
4A01.04 – Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
4A01.05 – Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
4A01.0Y – Other specified immunodeficiencies with predominantly antibody defects
4A01.0Z – Immunodeficiencies with predominantly antibody defects, unspecified

Foundation entity

Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells – http://id.who.int/icd/entity/1915135976

Part of: 4A01.0: Immunodeficiencies with predominantly antibody defects › 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system