4A01.04

ICD-11 MMS 2026-01

Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells

Index terms

  • Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
  • Recurrent infections associated with immunoglobulin isotypes deficiency
  • Recurrent infections associated with immunoglobulin isotypes
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  • Deficiency of immunoglobulin A with immunoglobulin G subclasses deficiency
  • Deficiency of IgA with IgG subclasses deficiency
  • Immunoglobulin heavy chain deficiency
  • Deficiency of IgG and/or IgA subclasses and/or IgE
  • K chain deficiency
  • Selective deficiency of immunoglobulin A
  • Selective deficiency of IgA
  • selective immunodeficiency of immunoglobulin A (IgA)
  • Selective deficiency of immunoglobulin G subclasses
  • IgG subclass deficiency
  • Selective deficiency of IgG subclasses
  • immunoglobin g subclass deficiency
  • immunoglobulin g subclass deficiency
  • selective IgG immunodeficiency
  • selective deficiency of IgG
  • selective immunoglobulin g deficiency
  • Selective deficiency of immunoglobulin M
  • Selective deficiency of IgM
  • selective IgM immunodeficiency
  • selective immunodeficiency of immunoglobulin M (IgM)

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A01.00 – Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
  • 4A01.01 – Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
  • 4A01.02 – Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
  • 4A01.03 – Transient hypogammaglobulinaemia of infancy
  • 4A01.05 – Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
  • 4A01.0Y – Other specified immunodeficiencies with predominantly antibody defects
  • 4A01.0Z – Immunodeficiencies with predominantly antibody defects, unspecified

Foundation entity

Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells – http://id.who.int/icd/entity/14210665

Part of: 4A01.0: Immunodeficiencies with predominantly antibody defects › 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system