Immunodeficiencies with predominantly antibody defects

Child codes

• 4A01.00 – Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
• 4A01.01 – Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
• 4A01.02 – Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
• 4A01.03 – Transient hypogammaglobulinaemia of infancy
• 4A01.04 – Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
• 4A01.05 – Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
• 4A01.0Y – Other specified immunodeficiencies with predominantly antibody defects
• 4A01.0Z – Immunodeficiencies with predominantly antibody defects, unspecified

Sibling codes

• 4A01.1 – Combined immunodeficiencies
• 4A01.2 – Diseases of immune dysregulation
• 4A01.3 – Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
• 4A01.Z – Primary immunodeficiencies due to disorders of adaptive immunity, unspecified

Foundation entity

Immunodeficiencies with predominantly antibody defects – http://id.who.int/icd/entity/85074116