4A42.0

ICD-11 MMS 2026-01

Paediatric onset systemic sclerosis

Description

Systemic sclerosis arising before the age of 16. Involvement of internal organs is less common but arthritis and myositis are more common than in adults.

Index terms

  • Paediatric onset systemic sclerosis
  • Diffuse paediatric systemic sclerosis
  • Limited paediatric systemic sclerosis

Exclusions from above levels

  • EB61.0 – Circumscribed scleroderma
  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 20 – Developmental anomalies

Sibling codes

  • 4A42.1 – Diffuse systemic sclerosis
  • 4A42.2 – Limited systemic sclerosis
  • 4A42.Z – Systemic sclerosis, unspecified

Foundation entity

Paediatric onset systemic sclerosis – http://id.who.int/icd/entity/2338375

Part of: 4A42: Systemic sclerosis › 04: Diseases of the immune system