4A42.2

ICD-11 MMS 2026-01

Limited systemic sclerosis

Description

Combination of calcinosis, Raynaud phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasia.

Index terms

  • Limited systemic sclerosis
  • CREST - [calcinosis, Raynaud phenomenon, oesophageal dysmotility, sclerodactyly, and telangiectasia] syndrome
  • CRST - [calcinosis, Raynaud phenomenon, sclerodactyly and telangiectasia] syndrome

Exclusions from above levels

  • EB61.0 – Circumscribed scleroderma
  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 20 – Developmental anomalies

Sibling codes

  • 4A42.0 – Paediatric onset systemic sclerosis
  • 4A42.1 – Diffuse systemic sclerosis
  • 4A42.Z – Systemic sclerosis, unspecified

Foundation entity

Limited systemic sclerosis – http://id.who.int/icd/entity/187455179

Part of: 4A42: Systemic sclerosis › 04: Diseases of the immune system