Diffuse systemic sclerosis

Description

Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc) characterised by truncal and acral skin fibrosis with an early and significant incidence of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse gastrointestinal disease, and myocardial involvement).

Index terms

Diffuse systemic sclerosis
Progressive systemic sclerosis

Exclusions from above levels

EB61.0 – Circumscribed scleroderma
02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium

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20 – Developmental anomalies

Sibling codes

4A42.0 – Paediatric onset systemic sclerosis
4A42.2 – Limited systemic sclerosis
4A42.Z – Systemic sclerosis, unspecified

Foundation entity

Diffuse systemic sclerosis – http://id.who.int/icd/entity/1852283743

Part of: 4A42: Systemic sclerosis › 04: Diseases of the immune system