4A44.A0ICD-11 MMS 2026-01
Microscopic polyangiitis
Description
Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, or arterioles). Necrotizing arteritis involving small and medium sized arteries may be present. Necrotizing glomerulonephritis is very common. Pulmonary capillaritis often occurs. Granulomatous inflammation is absent.
Index terms
- Microscopic polyangiitis
- MPA
- Microscopic polyarteritis
Inclusions
- Microscopic polyarteritis
Excludes
4A44.4– Polyarteritis nodosa
Exclusions from above levels
Sibling codes
Foundation entity
Microscopic polyangiitis – http://id.who.int/icd/entity/999231798
Part of: 4A44.A: Antineutrophil cytoplasmic antibody-associated vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system