4A44.A0

ICD-11 MMS 2026-01

Microscopic polyangiitis

Description

Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, or arterioles). Necrotizing arteritis involving small and medium sized arteries may be present. Necrotizing glomerulonephritis is very common. Pulmonary capillaritis often occurs. Granulomatous inflammation is absent.

Index terms

  • Microscopic polyangiitis
  • MPA
  • Microscopic polyarteritis

Inclusions

  • Microscopic polyarteritis

Excludes

  • 4A44.4 – Polyarteritis nodosa

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A44.A1 – Granulomatosis with polyangiitis
  • 4A44.A2 – Eosinophilic granulomatosis with polyangiitis
  • 4A44.AY – Other specified antineutrophil cytoplasmic antibody-associated vasculitis
  • 4A44.AZ – Antineutrophil cytoplasmic antibody-associated vasculitis, unspecified

Foundation entity

Microscopic polyangiitis – http://id.who.int/icd/entity/999231798

Part of: 4A44.A: Antineutrophil cytoplasmic antibody-associated vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system