Granulomatosis with polyangiitis

Description

Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common.

Index terms

Granulomatosis with polyangiitis
Wegener granulomatosis
Necrotising respiratory granulomatosis

Inclusions

Wegener granulomatosis

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A44.A0 – Microscopic polyangiitis
4A44.A2 – Eosinophilic granulomatosis with polyangiitis
4A44.AY – Other specified antineutrophil cytoplasmic antibody-associated vasculitis
4A44.AZ – Antineutrophil cytoplasmic antibody-associated vasculitis, unspecified

Foundation entity

Granulomatosis with polyangiitis – http://id.who.int/icd/entity/1020056159

Part of: 4A44.A: Antineutrophil cytoplasmic antibody-associated vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system