4A44.A2

ICD-11 MMS 2026-01

Eosinophilic granulomatosis with polyangiitis

Description

Eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels, and associated with asthma and eosinophilia. ANCA is most frequent when glomerulonephritis is present. (Arthritis Rheum 1990;33:1094-1100)

Index terms

  • Eosinophilic granulomatosis with polyangiitis
  • Allergic granulomatous angiitis
  • Churg-Strauss syndrome
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  • Churg-Strauss vasculitis

Inclusions

  • Churg-Strauss syndrome

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A44.A0 – Microscopic polyangiitis
  • 4A44.A1 – Granulomatosis with polyangiitis
  • 4A44.AY – Other specified antineutrophil cytoplasmic antibody-associated vasculitis
  • 4A44.AZ – Antineutrophil cytoplasmic antibody-associated vasculitis, unspecified

Foundation entity

Eosinophilic granulomatosis with polyangiitis – http://id.who.int/icd/entity/835880885

Part of: 4A44.A: Antineutrophil cytoplasmic antibody-associated vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system