ICD-11 MMS 2026-01
Hyperlipoproteinaemia
Description
Disorders of lipoprotein metabolism that result in high levels of lipoproteins in the circulating blood
Exclusions from above levels
5C56.0 – Sphingolipidosis3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency5A71.01 – Congenital adrenal hyperplasia
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5A81.1 – 5-alpha-reductase deficiencyLD28.01 – Marfan syndromeLD28.1 – Ehlers-Danlos syndromeLD2A.4 – androgen resistance syndrome18 – Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Child codes
5C80.0 – Hypercholesterolaemia5C80.1 – Hypertriglyceridaemia5C80.2 – Mixed hyperlipidaemia5C80.3 – Hyperalphalipoproteinaemia5C80.Y – Other specified hyperlipoproteinaemia5C80.Z – Hyperlipoproteinaemia, unspecified
Sibling codes
5C81 – Hypolipoproteinaemia5C8Y – Other specified disorders of lipoprotein metabolism or lipidaemias5C8Z – Unspecified disorders of lipoprotein metabolism or lipidaemias
Allowed postcoordination axes
Part of: 05: Endocrine, nutritional or metabolic diseases