Hereditary amyloidosis

Description

Hereditary amyloidosis (familial amyloidosis) is an inherited disorder that often affects the liver, nerves, heart and kidneys. Many different types of gene abnormalities present at birth are associated with an increased risk of amyloid disease. The type and location of an amyloid gene abnormality can affect the risk of certain complications, the age at which symptoms first appear, and the way the disease progresses over time.

Exclusions from above levels

• 6D80 – Dementia due to Alzheimer disease
• 2B31.2 – histiocytosis X (chronic)
• 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency