8A00.1

ICD-11 MMS 2026-01

Atypical parkinsonism

Description

Atypical parkinsonism is a term used to describe several neurodegenerative conditions where the degeneration extends beyond the substantia nigra and is more extensive than seen in conditions like Parkinson disease. The clinical picture is often more complex than PD and patients may have apraxia, supranuclear ophthalmoplegia or autonomic failure.

Exclusions from above levels

  • http://id.who.int/icd/entity/1425591047 – Myasthenia gravis or certain specified neuromuscular junction disorders
  • http://id.who.int/icd/entity/1525792972 – Arthropathies
  • 6A06 – Stereotyped movement disorder
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  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A00.10 – Progressive supranuclear palsy
  • 8A00.1Y – Other specified atypical parkinsonism
  • 8A00.1Z – Atypical parkinsonism, unspecified

Foundation children elsewhere

  • 8A22 – Lewy body disease
  • 8D87.01 – Multiple system atrophy, Parkinsonism

Sibling codes

  • 8A00.0 – Parkinson disease
  • 8A00.2 – Secondary parkinsonism
  • 8A00.3 – Functional parkinsonism
  • 8A00.Y – Other specified parkinsonism
  • 8A00.Z – Parkinsonism, unspecified

Foundation entity

Atypical parkinsonism – http://id.who.int/icd/entity/598493320

Allowed postcoordination axes

Part of: 8A00: Parkinsonism › 08: Diseases of the nervous system