8C74.11

ICD-11 MMS 2026-01

Hyperkalaemic periodic paralysis

Description

Hyperkalaemic periodic paralysis (HyperPP) is a muscle disorder characterised by episodic attacks of muscle weakness associated with an increase in serum potassium concentration.

Index terms

  • Hyperkalaemic periodic paralysis
  • Sodium channel disorders of muscles
  • adynamia episodica hereditaria
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  • hyperkalaemic periodic paralysis
  • sodium-responsive periodic paralysis
  • Normokalaemic periodic paralysis
  • normokalaemic periodic paralysis

Exclusions from above levels

  • http://id.who.int/icd/entity/155258022 – Metabolic disorders
  • LD26.41 – Arthrogryposis multiplex congenita
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8C74.10 – Hypokalaemic periodic paralysis
  • 8C74.1Y – Other specified periodic paralysis
  • 8C74.1Z – Periodic paralysis, unspecified

Foundation entity

Hyperkalaemic periodic paralysis – http://id.who.int/icd/entity/1308452752

Part of: 8C74.1: Periodic paralysis › 8C74: Periodic paralyses or disorders of muscle membrane excitability › 08: Diseases of the nervous system