LA07.3

ICD-11 MMS 2026-01

Primary syringomyelia or hydromyelia

Description

A condition caused by failure of the spinal canal to correctly develop during the antenatal period. This condition is characterised by a cavity within the spinal cord in which cerebrospinal fluid can accumulate. Confirmation is through observation of a fluid filled cavity within the spinal cord by imaging.

Index terms

  • Primary syringomyelia or hydromyelia
  • Congenital syringomyelia or hydromyelia
  • Congenital hydromyelia
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  • Hydromyelia
  • Hydrorachis
  • Primary syringomyelia

Excludes

  • 8D66.0 – Idiopathic syringomyelia
  • 8D66.1 – Syringomyelia due to certain specified cause
  • 8D66.Z – Syringomyelia

Exclusions from above levels

  • http://id.who.int/icd/entity/733825440 – Inborn errors of metabolism

Sibling codes

  • LA07.0 – Primary tethered cord syndrome
  • LA07.1 – Diastematomyelia
  • LA07.2 – Amyelia
  • LA07.4 – Arnold-Chiari malformation type I
  • LA07.Y – Other specified structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
  • LA07.Z – Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column, unspecified

Foundation entity

Primary syringomyelia or hydromyelia – http://id.who.int/icd/entity/465198086

Part of: LA07: Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column › 20: Developmental anomalies