BC65.1

ICD-11 MMS 2026-01

Brugada syndrome

Description

Clinical manifestations of cardiac syncope, ventricular tachycardia, ventricular fibrillation, or sudden death in conjunction with a genetic mutation associated with Brugada Syndrome and/or a Brugada pattern ECG (spontaneous or provoked).

Index terms

  • Brugada syndrome
  • Brugada type Idiopathic ventricular fibrillation
  • SUNDS - [sudden unexplained nocturnal death syndrome]
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  • Sudden unexplained nocturnal death syndrome
  • Brugada Syndrome with spontaneous Brugada ECG pattern
  • Brugada Syndrome with provoked Brugada ECG pattern

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • BC65.0 – Long QT syndrome
  • BC65.2 – Short QT syndrome
  • BC65.3 – Early repolarisation syndrome
  • BC65.4 – Idiopathic ventricular fibrillation
  • BC65.5 – Catecholaminergic polymorphic ventricular tachycardia
  • BC65.Y – Other specified cardiac arrhythmia associated with genetic disorder
  • BC65.Z – Cardiac arrhythmia associated with genetic disorder, unspecified

Foundation entity

Brugada syndrome – http://id.who.int/icd/entity/1250136584

Part of: BC65: Cardiac arrhythmia associated with genetic disorder › 11: Diseases of the circulatory system