Short QT syndrome

Description

Familial short QT syndrome is a rare cardiac rhythm disorder that associates a short QT interval (QT and QTc 300 ms) on the surface electrocardiogram (ECG) with a high risk of syncope or sudden death due to malignant ventricular arrhythmia.

Index terms

Short QT syndrome
Familial short QT syndrome

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

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19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

BC65.0 – Long QT syndrome
BC65.1 – Brugada syndrome
BC65.3 – Early repolarisation syndrome
BC65.4 – Idiopathic ventricular fibrillation
BC65.5 – Catecholaminergic polymorphic ventricular tachycardia
BC65.Y – Other specified cardiac arrhythmia associated with genetic disorder
BC65.Z – Cardiac arrhythmia associated with genetic disorder, unspecified

Foundation entity

Short QT syndrome – http://id.who.int/icd/entity/553392015

Part of: BC65: Cardiac arrhythmia associated with genetic disorder › 11: Diseases of the circulatory system