CB05.1

ICD-11 MMS 2026-01

Interstitial lung diseases associated with connective tissue diseases

Description

Interstitial lung diseases associated with connective tissue diseases refers to a group of lung diseases affecting the interstitium (the tissue and space around the air sacs of the lungs) associated with connective tissue diseases.

Index terms

  • Interstitial lung diseases associated with connective tissue diseases
  • Respiratory disorders in idiopathic inflammatory myopathies
  • Respiratory disorders in juvenile dermatomyositis
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  • Respiratory disorders in juvenile idiopathic arthritis
  • Respiratory disorders in mixed connective tissue disease
  • Respiratory disorders in other dermatomyositis
  • Respiratory disorders in polymyositis
  • Respiratory disorders in rheumatoid arthritis
  • rheumatoid arthritis with respiratory disorder
  • rheumatoid lung disease
  • Respiratory disorders in Sjögren syndrome
  • Sicca syndrome with lung involvement
  • Sjögren syndrome with lung involvement
  • Respiratory disorders in systemic lupus erythematosus
  • Respiratory disorders in systemic sclerosis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB05.0 – Diffuse alveolar damage
  • CB05.2 – Interstitial lung diseases associated with granulomatous diseases
  • CB05.3 – Interstitial lung diseases associated with metabolic diseases
  • CB05.4 – Interstitial lung diseases associated with systemic vasculitides
  • CB05.5 – Secondary pulmonary haemosiderosis
  • CB05.Y – Other specified interstitial lung diseases associated with systemic diseases
  • CB05.Z – Interstitial lung diseases associated with systemic diseases, unspecified

Foundation entity

Interstitial lung diseases associated with connective tissue diseases – http://id.who.int/icd/entity/1294786485

Allowed postcoordination axes

Part of: CB05: Interstitial lung diseases associated with systemic diseases › 12: Diseases of the respiratory system