CB05.5

ICD-11 MMS 2026-01

Secondary pulmonary haemosiderosis

Description

Secondary pulmonary hemosiderosis is a respiratory disease due to the deposition of hemosiderin-laden macrophages in lungs as a result of repeated alveolar haemorrhage secondary to another disease, especially dysimmunitary disorders (i.e. Heiner syndrome, autoimmune diseases), thrombotic disorders and cardiovascular disorders such as mitral stenosis. It manifests as a triad of haemoptysis, anaemia and diffuse parenchymal infiltrates on chest radiography

Index terms

  • Secondary pulmonary haemosiderosis
  • Heiner syndrome

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB05.0 – Diffuse alveolar damage
  • CB05.1 – Interstitial lung diseases associated with connective tissue diseases
  • CB05.2 – Interstitial lung diseases associated with granulomatous diseases
  • CB05.3 – Interstitial lung diseases associated with metabolic diseases
  • CB05.4 – Interstitial lung diseases associated with systemic vasculitides
  • CB05.Y – Other specified interstitial lung diseases associated with systemic diseases
  • CB05.Z – Interstitial lung diseases associated with systemic diseases, unspecified

Foundation entity

Secondary pulmonary haemosiderosis – http://id.who.int/icd/entity/878618614

Allowed postcoordination axes

Part of: CB05: Interstitial lung diseases associated with systemic diseases › 12: Diseases of the respiratory system