CB05.3

ICD-11 MMS 2026-01

Interstitial lung diseases associated with metabolic diseases

Description

Interstitial lung diseases associated with metabolic diseases refers to a group of lung diseases affecting the interstitium (the tissue and space around the air sacs of the lungs). This diagnosis is associated with a large class of genetic diseases involving disorders of metabolism.

Index terms

  • Interstitial lung diseases associated with metabolic diseases
  • Interstitial lung disease in Gaucher disease
  • Interstitial lung disease in Niemann-Pick disease
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  • Interstitial lung disease in protein intolerance

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Foundation children elsewhere

  • 5A51.2 – Familial hypocalciuric hypercalcaemia

Sibling codes

  • CB05.0 – Diffuse alveolar damage
  • CB05.1 – Interstitial lung diseases associated with connective tissue diseases
  • CB05.2 – Interstitial lung diseases associated with granulomatous diseases
  • CB05.4 – Interstitial lung diseases associated with systemic vasculitides
  • CB05.5 – Secondary pulmonary haemosiderosis
  • CB05.Y – Other specified interstitial lung diseases associated with systemic diseases
  • CB05.Z – Interstitial lung diseases associated with systemic diseases, unspecified

Foundation entity

Interstitial lung diseases associated with metabolic diseases – http://id.who.int/icd/entity/1766776408

Allowed postcoordination axes

Part of: CB05: Interstitial lung diseases associated with systemic diseases › 12: Diseases of the respiratory system