CB06

ICD-11 MMS 2026-01

Pulmonary alveolar microlithiasis

Description

Pulmonary alveolar microlithiasis is an idiopathic rare disease in which concretions composed of calcium and phosphorus collect in alveolar spaces. A systemic disorder of calcium metabolism has not been identified, and the serum calcium and phosphate levels are normal. Cough and dyspnoea are the most common presenting symptoms. Expectorated microliths have been reported. Inspiratory crackles, finger clubbing, and signs of cor pulmonale may be present in more advanced disease.

Index terms

  • Pulmonary alveolar microlithiasis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB00 – Acute respiratory distress syndrome
  • CB01 – Pulmonary oedema
  • CB02 – Pulmonary eosinophilia
  • CB03 – Idiopathic interstitial pneumonitis
  • CB04 – Primary interstitial lung diseases specific to infancy or childhood
  • CB05 – Interstitial lung diseases associated with systemic diseases
  • CB07 – Lymphangioleiomyomatosis
  • CB0Y – Other specified respiratory diseases principally affecting the lung interstitium
  • CB0Z – Respiratory diseases principally affecting the lung interstitium, unspecified

Foundation entity

Pulmonary alveolar microlithiasis – http://id.who.int/icd/entity/1220010076

Part of: 12: Diseases of the respiratory system