CB06ICD-11 MMS 2026-01
Pulmonary alveolar microlithiasis
Description
Pulmonary alveolar microlithiasis is an idiopathic rare disease in which concretions composed of calcium and phosphorus collect in alveolar spaces. A systemic disorder of calcium metabolism has not been identified, and the serum calcium and phosphate levels are normal. Cough and dyspnoea are the most common presenting symptoms. Expectorated microliths have been reported. Inspiratory crackles, finger clubbing, and signs of cor pulmonale may be present in more advanced disease.
Index terms
- Pulmonary alveolar microlithiasis
Exclusions from above levels
Sibling codes
CB00– Acute respiratory distress syndromeCB01– Pulmonary oedemaCB02– Pulmonary eosinophiliaCB03– Idiopathic interstitial pneumonitisCB04– Primary interstitial lung diseases specific to infancy or childhoodCB05– Interstitial lung diseases associated with systemic diseasesCB07– LymphangioleiomyomatosisCB0Y– Other specified respiratory diseases principally affecting the lung interstitiumCB0Z– Respiratory diseases principally affecting the lung interstitium, unspecified
Foundation entity
Pulmonary alveolar microlithiasis – http://id.who.int/icd/entity/1220010076
Part of: 12: Diseases of the respiratory system