Lymphangioleiomyomatosis

Description

Lymphangioleiomyomatosis (LAM) is a multiple cystic lung disease characterised by progressive cystic destruction of the lung and lymphatic abnormalities, frequently associated with renal angiomyolipomas (AMLs). LAM occurs either sporadically or as a manifestation of tuberous sclerosis complex (TSC).

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

Show allHide

19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations and chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes

Child codes

CB07.0 – Lymphangioleiomyomatosis associated with tuberous sclerosis complex
CB07.1 – Sporadic lymphangioleiomyomatosis
CB07.Y – Other specified lymphangioleiomyomatosis
CB07.Z – Lymphangioleiomyomatosis, unspecified

Sibling codes

CB00 – Acute respiratory distress syndrome
CB01 – Pulmonary oedema
CB02 – Pulmonary eosinophilia
CB03 – Idiopathic interstitial pneumonitis
CB04 – Primary interstitial lung diseases specific to infancy or childhood
CB05 – Interstitial lung diseases associated with systemic diseases
CB06 – Pulmonary alveolar microlithiasis
CB0Y – Other specified respiratory diseases principally affecting the lung interstitium
CB0Z – Respiratory diseases principally affecting the lung interstitium, unspecified

Foundation entity

Lymphangioleiomyomatosis – http://id.who.int/icd/entity/902628446

Part of: 12: Diseases of the respiratory system